Study Set Content:
Protein synthesis in cells around the
body
Making nonessential amino acids needed for
protein synthesis
Making other (blank) compounds
nitrogen-containing
• Rearranged and stored as
fat
is there any storage form of protein
no
Rearranged into glucose for fuel for the
brain and red blood cells
Metabolized as fuel, for an immediate source of
ATP
e is a set of biochemical reactions that produces urea from ammonia in order to prevent a toxic level of ammonia in the body.
The urea cycle
Because ammonia is toxic, the liver transforms it into
urea
Urea is then transported to the kidneys and excreted in the
urine
Prior to the urea cycle, ammonia is produced from the breakdown of
amino acids
Hyperammonemia type Defective enzyme
CPS I
Hyperammonemia type II
Ornithine transcarbamylase
Citrullinemia
Arginosuccinate Synthase
Argininosuccinic aciduria
Argininosuccinate Lyase
Arginemia
Arginase
Hyperammonemia type I produce excessive amounts of
ammonia
Hyperammonemia type II
ammonia
Citrullinemia
citrulline
Argininosuccinic aciduria
Arginosuccinate
